Amniotic  band  syndrome  as  a  cause  of  ectopia  cordis  thoracalis  and  other  craniofacial  defects

Megha Kumra; Sushil G. Kachewar; Dilip L. Lakhkar

doi:10.5455/IJMRCR.amniotic-band-syndrome-ectopia-cordis-thoracalis

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Case Report

Online Publishing Date:
31 / 01 / 2019

Int J Med Rev Case Rep. 2019; 3(8): 513-517

doi: 10.5455/IJMRCR.amniotic-band-syndrome-ectopia-cordis-thoracalis

Amniotic band syndrome as a cause of ectopia cordis thoracalis and other craniofacial defects

Megha Kumra, Sushil G. Kachewar, Dilip L. Lakhkar.

Abstract
A 24 week gestation fetus, on ultrasound, was found to have Ectopia Cordis, besides other anomalies like frontonasal dysgenesis, facial cleft, hydrocephalus and a distorted skull vault. Fibrous bands were seen to be attached to the apex of the heart, face, and placenta. Isolated Ectopia Cordis occurs due to malformed thoracic chest wall during early embryogenesis. However, fibrous bands adherent to the heart causing mechanical forces may also lead to ectopia cordis, referred to as mechanical teratogenesis. These amniotic bands are formed due to early rupture of chorion or amnion in embryogenesis and a spectrum of defects is found following it, the variety of which is based upon the timing of rupture. As is illustrated by our ultrasound pictures and clinical specimens, a cephalic pointing cardiac apex secondary to tethering of the heart to frontonasal region of face by amniotic bands could be the etiology of this thoracoabdominal ectopia cordis Thus Ectopia cordis with amniotic bands appears to have an etiology entirely different from isolated ectopia cordis. This suggests distinct etiologies for ectopia cordis and in the light of literature, they have been discussed with this case report

Key words: ectopia cordis, amniotic band syndrome, mechanical teratogenesis

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Pubmed Style

Kumra M, Kachewar SG, Lakhkar DL. Amniotic band syndrome as a cause of ectopia cordis thoracalis and other craniofacial defects. Int J Med Rev Case Rep. 2019; 3(8): 513-517. doi:10.5455/IJMRCR.amniotic-band-syndrome-ectopia-cordis-thoracalis

Web Style

Kumra M, Kachewar SG, Lakhkar DL. Amniotic band syndrome as a cause of ectopia cordis thoracalis and other craniofacial defects. https://www.mdpub.net/?mno=20799 [Access: April 04, 2024]. doi:10.5455/IJMRCR.amniotic-band-syndrome-ectopia-cordis-thoracalis

AMA (American Medical Association) Style

Kumra M, Kachewar SG, Lakhkar DL. Amniotic band syndrome as a cause of ectopia cordis thoracalis and other craniofacial defects. Int J Med Rev Case Rep. 2019; 3(8): 513-517. doi:10.5455/IJMRCR.amniotic-band-syndrome-ectopia-cordis-thoracalis

Vancouver/ICMJE Style

Kumra M, Kachewar SG, Lakhkar DL. Amniotic band syndrome as a cause of ectopia cordis thoracalis and other craniofacial defects. Int J Med Rev Case Rep. (2019), [cited April 04, 2024]; 3(8): 513-517. doi:10.5455/IJMRCR.amniotic-band-syndrome-ectopia-cordis-thoracalis

Harvard Style

Kumra, M., Kachewar, . S. G. & Lakhkar, . D. L. (2019) Amniotic band syndrome as a cause of ectopia cordis thoracalis and other craniofacial defects. Int J Med Rev Case Rep, 3 (8), 513-517. doi:10.5455/IJMRCR.amniotic-band-syndrome-ectopia-cordis-thoracalis

Turabian Style

Kumra, Megha, Sushil G. Kachewar, and Dilip L. Lakhkar. 2019. Amniotic band syndrome as a cause of ectopia cordis thoracalis and other craniofacial defects. International Journal of Medical Reviews and Case Reports, 3 (8), 513-517. doi:10.5455/IJMRCR.amniotic-band-syndrome-ectopia-cordis-thoracalis

Chicago Style

Kumra, Megha, Sushil G. Kachewar, and Dilip L. Lakhkar. "Amniotic band syndrome as a cause of ectopia cordis thoracalis and other craniofacial defects." International Journal of Medical Reviews and Case Reports 3 (2019), 513-517. doi:10.5455/IJMRCR.amniotic-band-syndrome-ectopia-cordis-thoracalis

MLA (The Modern Language Association) Style

Kumra, Megha, Sushil G. Kachewar, and Dilip L. Lakhkar. "Amniotic band syndrome as a cause of ectopia cordis thoracalis and other craniofacial defects." International Journal of Medical Reviews and Case Reports 3.8 (2019), 513-517. Print. doi:10.5455/IJMRCR.amniotic-band-syndrome-ectopia-cordis-thoracalis

APA (American Psychological Association) Style

Kumra, M., Kachewar, . S. G. & Lakhkar, . D. L. (2019) Amniotic band syndrome as a cause of ectopia cordis thoracalis and other craniofacial defects. International Journal of Medical Reviews and Case Reports, 3 (8), 513-517. doi:10.5455/IJMRCR.amniotic-band-syndrome-ectopia-cordis-thoracalis

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