E-ISSN 2534-9821
 

Case Report
Online Published: 06 Jul 2020
 


Anesthetic management for tethered cord syndrome in a child with Emanuel syndrome

Yeliz Kılıç, Murat Vural, Mehmet Sacit Güleç.


Abstract
Background: Emanuel syndrome (ES) is a rare hereditary disorder characterized by growth and mental retardation, congenital malformations, and craniofacial anomalies. There is limited data on the anesthetic management of this syndrome, all of which come from case reports. Report: A 7-year-old girl presented with urinary incontinence caused by tethered cord syndrome. Laminoplasty plus transection of the tight filum terminale to release the tethered conus medullaris under total intravenous anesthesia was performed. Discussion: Anesthesia management of patients with ES requires special attention due to the airway difficulties associated with micrognathia and palate anomalies and accompanying congenital malformations that primarily affect cardiovascular and neurologic systems. Monitoring the cardiac parameters and neurological signs during the surgery is of great importance for the patient safety. Conclusion: This case report is the first demonstrating total intravenous anesthesia in patients with ES, and may help to guide anesthesiologists in the anesthetic management of these patients.

Key words: Airway management, total intravenous anesthesia, difficult intubation, Emanuel syndrome


 
ARTICLE TOOLS
Abstract
PDF Fulltext
How to cite this articleHow to cite this article
Citation Tools
Related Records
 Articles by Yeliz Kılıç
Articles by Murat Vural
Articles by Mehmet Sacit Güleç
on Google
on Google Scholar


How to Cite this Article
Pubmed Style

Kılıc Y, Vural M, Gulec MS. Anesthetic management for tethered cord syndrome in a child with Emanuel syndrome. Int J Med Rev Case Rep. 2020; 4(12): 46-47. doi:10.5455/IJMRCR.tethered-cord-syndrome-child


Web Style

Kılıc Y, Vural M, Gulec MS. Anesthetic management for tethered cord syndrome in a child with Emanuel syndrome. https://www.mdpub.net/?mno=21440 [Access: October 13, 2024]. doi:10.5455/IJMRCR.tethered-cord-syndrome-child


AMA (American Medical Association) Style

Kılıc Y, Vural M, Gulec MS. Anesthetic management for tethered cord syndrome in a child with Emanuel syndrome. Int J Med Rev Case Rep. 2020; 4(12): 46-47. doi:10.5455/IJMRCR.tethered-cord-syndrome-child



Vancouver/ICMJE Style

Kılıc Y, Vural M, Gulec MS. Anesthetic management for tethered cord syndrome in a child with Emanuel syndrome. Int J Med Rev Case Rep. (2020), [cited October 13, 2024]; 4(12): 46-47. doi:10.5455/IJMRCR.tethered-cord-syndrome-child



Harvard Style

Kılıc, Y., Vural, . M. & Gulec, . M. S. (2020) Anesthetic management for tethered cord syndrome in a child with Emanuel syndrome. Int J Med Rev Case Rep, 4 (12), 46-47. doi:10.5455/IJMRCR.tethered-cord-syndrome-child



Turabian Style

Kılıc, Yeliz, Murat Vural, and Mehmet Sacit Gulec. 2020. Anesthetic management for tethered cord syndrome in a child with Emanuel syndrome. International Journal of Medical Reviews and Case Reports, 4 (12), 46-47. doi:10.5455/IJMRCR.tethered-cord-syndrome-child



Chicago Style

Kılıc, Yeliz, Murat Vural, and Mehmet Sacit Gulec. "Anesthetic management for tethered cord syndrome in a child with Emanuel syndrome." International Journal of Medical Reviews and Case Reports 4 (2020), 46-47. doi:10.5455/IJMRCR.tethered-cord-syndrome-child



MLA (The Modern Language Association) Style

Kılıc, Yeliz, Murat Vural, and Mehmet Sacit Gulec. "Anesthetic management for tethered cord syndrome in a child with Emanuel syndrome." International Journal of Medical Reviews and Case Reports 4.12 (2020), 46-47. Print. doi:10.5455/IJMRCR.tethered-cord-syndrome-child



APA (American Psychological Association) Style

Kılıc, Y., Vural, . M. & Gulec, . M. S. (2020) Anesthetic management for tethered cord syndrome in a child with Emanuel syndrome. International Journal of Medical Reviews and Case Reports, 4 (12), 46-47. doi:10.5455/IJMRCR.tethered-cord-syndrome-child