E-ISSN 2534-9821
 

Case Report

Online Publishing Date:
02 / 03 / 2020

 


Acute Demyelinating Encephalomyelitis(ADEM) Presenting With Dystonia

A. Bruce Janati, Suliman Almisned, Naif Alghasab, Kareemah Salem Al-Shurtan, Ahmad Abdullah.


Abstract
Introduction: Acute disseminated encephalomyelitis (ADEM) is a monophasic autoimmune inflammatory demyelinating disease of the central nervous system that predominantly involves the white matter of the brain and spinal cord(1). It is a rare disease affecting both children and adults (2). In the majority of cases ADEM usually appears after vaccinations or viral/bacterial infections
Methods: This was a case study of two patients with ADEM presenting with dystonia. The study was conducted at King Khalid Hospital in Hail, Saudi Arabia.
Results: MRI studies showed subcortical white matter lesion in the right frontal region in patient 1, and a right thalamic lesion in patient 2.
Conclusion: We conclude that the lesions detected by the MRI were responsible for the limb dystonia. We believe that the lesions seriously disrupted the cortical-striatal pathways in the right cerebral hemisphere, leading to hemi-dystonia.

Key words: Acute Demyelinating Encephalomyelitis(ADEM), Dystonia


 
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How to Cite this Article
Pubmed Style

Janati AB, Almisned S, Alghasab N, Al-Shurtan KS, Abdullah A. Acute Demyelinating Encephalomyelitis(ADEM) Presenting With Dystonia. Int J Med Rev Case Rep. 2020; 4(4): 116-118. doi:10.5455/IJMRCR.Acute-Demyelinating-Encephalomyelitis


Web Style

Janati AB, Almisned S, Alghasab N, Al-Shurtan KS, Abdullah A. Acute Demyelinating Encephalomyelitis(ADEM) Presenting With Dystonia. https://www.mdpub.net/?mno=86388 [Access: April 04, 2024]. doi:10.5455/IJMRCR.Acute-Demyelinating-Encephalomyelitis


AMA (American Medical Association) Style

Janati AB, Almisned S, Alghasab N, Al-Shurtan KS, Abdullah A. Acute Demyelinating Encephalomyelitis(ADEM) Presenting With Dystonia. Int J Med Rev Case Rep. 2020; 4(4): 116-118. doi:10.5455/IJMRCR.Acute-Demyelinating-Encephalomyelitis



Vancouver/ICMJE Style

Janati AB, Almisned S, Alghasab N, Al-Shurtan KS, Abdullah A. Acute Demyelinating Encephalomyelitis(ADEM) Presenting With Dystonia. Int J Med Rev Case Rep. (2020), [cited April 04, 2024]; 4(4): 116-118. doi:10.5455/IJMRCR.Acute-Demyelinating-Encephalomyelitis



Harvard Style

Janati, A. B., Almisned, . S., Alghasab, . N., Al-Shurtan, . K. S. & Abdullah, . A. (2020) Acute Demyelinating Encephalomyelitis(ADEM) Presenting With Dystonia. Int J Med Rev Case Rep, 4 (4), 116-118. doi:10.5455/IJMRCR.Acute-Demyelinating-Encephalomyelitis



Turabian Style

Janati, A. Bruce, Suliman Almisned, Naif Alghasab, Kareemah Salem Al-Shurtan, and Ahmad Abdullah. 2020. Acute Demyelinating Encephalomyelitis(ADEM) Presenting With Dystonia. International Journal of Medical Reviews and Case Reports, 4 (4), 116-118. doi:10.5455/IJMRCR.Acute-Demyelinating-Encephalomyelitis



Chicago Style

Janati, A. Bruce, Suliman Almisned, Naif Alghasab, Kareemah Salem Al-Shurtan, and Ahmad Abdullah. "Acute Demyelinating Encephalomyelitis(ADEM) Presenting With Dystonia." International Journal of Medical Reviews and Case Reports 4 (2020), 116-118. doi:10.5455/IJMRCR.Acute-Demyelinating-Encephalomyelitis



MLA (The Modern Language Association) Style

Janati, A. Bruce, Suliman Almisned, Naif Alghasab, Kareemah Salem Al-Shurtan, and Ahmad Abdullah. "Acute Demyelinating Encephalomyelitis(ADEM) Presenting With Dystonia." International Journal of Medical Reviews and Case Reports 4.4 (2020), 116-118. Print. doi:10.5455/IJMRCR.Acute-Demyelinating-Encephalomyelitis



APA (American Psychological Association) Style

Janati, A. B., Almisned, . S., Alghasab, . N., Al-Shurtan, . K. S. & Abdullah, . A. (2020) Acute Demyelinating Encephalomyelitis(ADEM) Presenting With Dystonia. International Journal of Medical Reviews and Case Reports, 4 (4), 116-118. doi:10.5455/IJMRCR.Acute-Demyelinating-Encephalomyelitis